𝐌𝐨𝐫𝐧𝐢𝐧𝐠 𝐆𝐥𝐨𝐫𝐲 𝐒𝐲𝐧𝐝𝐫𝐨𝐦𝐞
● Rare congenital malformation of optic disc (1 in 10 million)
● When associated with systemic signs and symptoms→ morning glory syndrome
● Morphological similarity to the flower of the morning glory plant
● Sporadic condition
● More common in females
𝘊𝘰𝘮𝘮𝘰𝘯 𝘴𝘺𝘴𝘵𝘦𝘮𝘪𝘤 𝘢𝘴𝘴𝘰𝘤𝘪𝘢𝘵𝘪𝘰𝘯𝘴:
● Transsphenoidal basal encephalocele
● Midfacial malformations
● Others: Callosal agenesis, Hypoplasia of cerebral arteries, PHACE syndrome, Neurofibromatosis 2
𝘚𝘪𝘨𝘯𝘴 𝘢𝘯𝘥 𝘴𝘺𝘮𝘱𝘵𝘰𝘮𝘴:
● Visual acuity ranges from 20/20 to counting fingers depending on extent of optic nerve affected
● Visual field defect: Enlarged blind spot
● Associated Amblyopia, strabismus
𝘈𝘱𝘱𝘦𝘢𝘳𝘢𝘯𝘤𝘦:
● Usually unilateral
● Large funnel shaped excavation in optic disc
● White glial tissue occupying the central disc
● Increased number of abnormally straight retinal blood vessels arise from disc margin and run radially towards peripheral fundus
● Peripapillary chorioretinal pigmentation can be seen
● Macular capture: When macula is involved in the excavation
● Serous retinal detachment can occur in 30% (that tend to originate in peripapillary area and extend to posterior pole)
𝘋𝘋:
● Optic disc coloboma
● Peripapillary staphyloma
𝘔𝘢𝘯𝘢𝘨𝘦𝘮𝘦𝘯𝘵:
● Management of amblyopia, strabismus
● Observe for serous RDs
● Brain imaging to rule out CNS involvement
Image from Rajan Eye Care Hospital#ophthalmology#ophthal#doctor#health#medical#vision#education#optometry#medicalstudent#optometrist#medicine#eye#ophtho#ophthalmologist#ophthalmo#med#medicaleducation#ophthalmologyresident#ophthalmologyresidency#retina#opticdisc#fundus#morningglory#morningglorysyndrome#opticdisccoloboma#congenitalopticdiscanamoly
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